Desmoplastic small round cell tumor (DSCRCT)

What is Desmoplastic small round cell tumor?

Desmoplastic small round cell tumor (DSRCT) is a type of cancer. It is usually found in the belly, but rarely occurs in other parts of the body. Tumors are formed by small, round cancer cells and are surrounded by scar-like tissue. The tumor may not be found until the tumor has grown larger.

What causes Desmoplastic small round cell tumor? Who is affected?

The exact cause is unknown, but genetic factors play a role. It is most common in men and young boys. DSRCT can occur at any age.

What are the symptoms of Desmoplastic small round cell tumor?

Symptoms can include:

• Pain or a lump in the abdomen
• Cramping
• Nausea
• Vomiting
• Diarrhea
• Constipation
• Trouble having a bowel movement and/or passing gas
• Abdominal swelling

How is Desmoplastic small round cell tumor treated?

Since desmoplastic small round cell tumor is so rare, there is no standard treatment protocol. Some ways that desmoplastic can be treated include:

• Surgery
• Hyperthermic intraperitoneal chemotherapy (HIPEC)
• Chemotherapy
• Radiation Therapy